Cranio-Vertebral AnomaliesDR. ANKUR NANDAN VARSHNEY IMS, BHU Varanasi. Cranio vertebral anomalies- overview -. 1. DR. SUMIT KAMBLE SENIOR RESIDENT DEPT. OF NEUROLOGY GMC, KOTA; 2. ANATOMY OF. The craniovertebral junction is the most complex of the axial skeleton, residing between the skull and the upper cervical spine. Congenital, developmental, and .

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Ventromedial part of the somatomes migrate and cluster around notochord- Sclerotomes. Down’s syndrome lax joints. Segmentation falilure of C Twenty-two patients had previous posterior decompression and 27 had previous syrinx to subarachnoid shunt with delayed deterioration.

Craniovertebral junction anomalies – Knowledge for medical students and physicians

The critical sagittal canal diameter at the foramen magnum was 19 mm. Surgery is often indicated to prevent or treat neurological symptoms.

Proatlas remnants were identified in 8 and atlas assimilation in 92 patients. Treatment of basilar invagination by atlantoaxial joint distraction and direct lateral mass fixation. Prevalence appears to be high as observed by neurosurgeons in India although it is yet to be corroborated by epidemiological studies.

Caudal half joins with cephalic half of adjacent sclerotome anomaliex future vertebra Mesenchymal cells of the fissure condense to form I. X ray with chamberlin line, mcgregor line etc have become history. Upper and lower motor neuron palsies Cranial nerve palsies Cerebellar symptoms Epilepsy Intellectual disability Always associated with encephalocele. Removing anomalise compressing element form it front is more rationale.


Craniovertebral anomalies: Role for craniovertebral realignment Atul Goel Neurol India

MRI has totally changed the prospects of investigation of spinal lesions and more so at CV junction. Assimilation of atlas with the occiput is an expression of nonsegmentation of certain parts of the proatlas and fusion of the first spinal sclerotome with the proatlas.

In basilar invagination, there is crowding of structures in the small post. Symptomatic in infancy Breathing difficulties, including apneic episodes Feeding difficulties Always associated with myelomeningocele Features of syringomyelia or hydrocephalusif present.

It occurs in 0. Reduction of fixed atlantoaxial dislocation: Prepare and succeed on your medical exams. Mal aligned bony components of the spinal canal compress underlying cord due to dislocation of the joints, the commonest is Atlanto axial dislocation. Mirror movements of the hands are often seen in klippel Feil syndrome due to inadequate decussation of pyramidal tract at medulla. Failure of segmentation from occiput. Hartshell frame is still being used by many. Dens lacks a good nutrient artery.

Aplasia of atlas arches.

J Neurosurg Spine in press. A dysplastic odontoid provides a vulnerable situation.

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Open access journal indexed with Index Medicus. An injury in early childhood probably leads to Os-odontoideum in later life due to avascular necrosis. Sphincter disturbance is rare. Goel A, Achawal S. Anomalkes birth ctaniovertebral base is separate from the body of axis by cranniovertebral segment of cartilage which persists until the age of eight and the center gets ossified.


In early stages of A-A dislocations, most of them are reducible and require only stabilization. Goel A, Kulkarni AG. Irrespective of methods used it is essential to immobilize its CV junction with collar till bony fusion occurs, which may take 3 months.

Smaller number present with neck tilt, neck pain, cough headaches, occipital cephalalgia without any deficit. Ideal will be the Halo frame. Mostly fatal in early infancy For those that survive: Instances of redislocation by snapping of wire, anomaliess of screws are not rare. Clinical features of CVJ anomalies are due to compression of the brain stem and the spinal cord and may include recurrent occipital headaches, neck aches, bulbar palsyand upper and lower motor neuron palsy.

These are only few odontoid base falls to the above specification. In certain diseases of bone like hyperparathyroidism, pagets or osteomalacia, there is softening of the base of skull which gets invaginated.

Regional Anatomy, Pathology, and Traumatology. It appears that JavaScript is disabled in your browser.